Significats de marfan's syndrome en anglès

Background: Marfan's syndrome is characterized by progressive dilatation of the aortic root.

Aortic dissection rarely occurs in 2 or more family members without Marfan's syndrome.

In the descending aorta, however, aortic stiffness was increased only in patients with Marfan's syndrome.

Neither of 2 siblings nor other family members had any features of the Marfan's syndrome.

It is proposed that two aortic dissections occurred coincidentally in one family without Marfan's syndrome.

Literature on the anesthetic management of delivery in patients with Marfan's syndrome consists only of case reports.

Objective: To investigate dilatory changes of the aorta distal to the root in patients with Marfan's syndrome.

The medical literature is somewhat unclear whether sports participation is unsafe for all individuals with Marfan's syndrome.

PMID: 7933556 There was neither stigmata of Marfan's syndrome nor any sign of dissection of the ascending aorta or coronary arteries.

Methods: We reviewed the medical records of all pregnant women with Marfan's syndrome who were followed at their institution over a 6-year period.

Methods and results: Data of 268 patients with Marfan's syndrome who were enrolled in the Euro Heart Survey on adult congenital heart disease were analysed.

We therefore conducted a retrospective review of medical records focusing on anesthetic management of delivery in patients with Marfan's syndrome in a national referral center.