Background: Marfan'ssyndrome is characterized by progressive dilatation of the aortic root.
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Aortic dissection rarely occurs in 2 or more family members without Marfan'ssyndrome.
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In the descending aorta, however, aortic stiffness was increased only in patients with Marfan'ssyndrome.
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Neither of 2 siblings nor other family members had any features of the Marfan'ssyndrome.
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It is proposed that two aortic dissections occurred coincidentally in one family without Marfan'ssyndrome.
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Literature on the anesthetic management of delivery in patients with Marfan'ssyndrome consists only of case reports.
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Objective: To investigate dilatory changes of the aorta distal to the root in patients with Marfan'ssyndrome.
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The medical literature is somewhat unclear whether sports participation is unsafe for all individuals with Marfan'ssyndrome.
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PMID: 7933556 There was neither stigmata of Marfan'ssyndrome nor any sign of dissection of the ascending aorta or coronary arteries.
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Methods: We reviewed the medical records of all pregnant women with Marfan'ssyndrome who were followed at their institution over a 6-year period.
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Methods and results: Data of 268 patients with Marfan'ssyndrome who were enrolled in the Euro Heart Survey on adult congenital heart disease were analysed.
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We therefore conducted a retrospective review of medical records focusing on anesthetic management of delivery in patients with Marfan'ssyndrome in a national referral center.