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We introduce a narrative review of literature of somatostatinoma including the relationship with neurofibromatosis type 1.
2
Duodenal somatostatinoma is associated with the syndrome which actually involves more often a duodenal tumour of GIST type than a somatostatin secreting neoplasia.
3
Somatostatinoma, when not located on pancreas but in duodenoum, may be registered in subjects with neurofibromatosis type 1 most probably in addition to other tumours.
Translations for somatostatin-producing neuroendocrine tumor