A severe epilepsy syndrome with triad of infantile spasms, an interictal electroencephalogram (EEG) pattern termed hypsarrhythmia, and mental retardation.
A rare epileptic disorder in infants that is difficult to treat.
1 We retrospectively studied 18 patients with West syndrome treated with ACTH according to Fukuyama's method.
2 We experienced one symptomatic case and three cryptogenic cases of West syndrome that showed spontaneous remission.
3 Of these, 3 had West syndrome .
4 Generally, West syndrome is an intractable epileptic syndrome in infancy, although spontaneous remission has been reported in some cases.
5 Here, we report a patient with West syndrome whose chromosome analysis revealed 14q11.2-21.1 duplication.
6 An immunologic response to infection might be one of the factors involved in the remission of West syndrome , but the mechanisms remain unknown.
7 Our results suggest that choice of drug in the initial treatment of West syndrome should be determined by clinical features (especially etiology).
8 The changes in serum antibody values suggest that the spontaneous remission of West syndrome was related to human herpesvirus 6 and 7 infections.
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Esta colocación está formada por: Translations for west syndrome