Pyogenic arthritis-pyoderma gangrenosum-acne syndrome is a rare pleiotropic autoinflammatory disorder of childhood, primarily affecting the joints and skin.
It's fra the mon who finds it, and we own the location.
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She telled me my poor wench went to the workhouse fra there.
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He told me that Jimmy na held me responsible fra his death.
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But if ever woman died fra' a broken heart, there she lies.'
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Answer me, or 'fore God I'll wring the answer fra your body!
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TNFa blockade appears to be effective in treating the cutaneous manifestations of PAPAsyndrome.
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Neutrophil granule proteins are markedly elevated ex vivo and in the plasma, and elevated levels might be compatible with a diagnosis of PAPAsyndrome.
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Conclusion: This analysis of 5 patients demonstrates that mutations in PSTPIP1 are incompletely penetrant and variably expressed in the PAPAsyndrome.
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In exceptional cases, tuberculous joint disease follows an acute course resembling that of the pyogenicarthritis of infants.
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Right lung wedge biopsies via thoracostomy was performed and showed pulmonary pyodermagangrenosum.
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Rapid improvement of pyodermagangrenosum was seen within three doses of infliximab infusion.
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We report a case of scurvy manifesting as persistent non-healing lower-extremity ulcerations, initially mistaken for pyodermagangrenosum.
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It is particularly unusual for extracutaneous pyodermagangrenosum to manifest prior to skin findings and without an associated systemic disorder.
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This is the first case of pulmonary pyodermagangrenosum without any associated underlying systemic disorder and without any cutaneous manifestations to date.