Results: The study sample comprised 32 patients with uterine LMS.

Conclusion: Uterine LMS are rare and aggressive uterine neoplasms with high recurrence rates and metastatic potential.

Knowledge of lymph node status had minimal impact on the clinical management of women with uterine LMS and ESS.

Surgery consisting of total hysterectomy with or without bilateral salpingo-oophorectomy is the most important treatment-element in patients with uterine LMS.